0–11 years (n = 53) | 12–18 years (n = 29) | 19 + years (n = 58) | Total (n = 140) | |
---|---|---|---|---|
Type of hemophilia | ||||
Moderate | 256,970 (236,395 − 277,545) | 35,546 (35,546 − 35,546) | 129,622 (107,383–663,537) | 172,721 (96,264–277,545) |
Severe | 303,601 (15,099–514,529) | 540,633 (354,270–698,929) | 726,561 (359,276–996,386) | 488,948 (239,520–805,822) |
Presence of inhibitors | ||||
Yes | 505,898 (200,403–774,557) | 946,540 (836,118–1,056,961) | 864,048 (297,335–1,428,737) | 702,445 (202,677–1,055,373) |
No | 274,822 (157,536 − 365,392) | 513,056 (329,957 − 679,370) | 673,381 (286,092–967,392) | 440,753 (224,758 − 748,379) |
Bleeding | ||||
Yes | 267,015 (151,975 − 418,560) | 540,633 (310,776 − 673,856) | 782,214 (175,251–1,212,384) | 455,489 (204,485–974,735) |
No | 307,721 (162,310–522,012) | 513,056 (348,863 − 707,851) | 571,247 (406,028–918,320) | 446,174 (256,039–707,851) |
Target joints affected | ||||
Yes | 514,529 (342,690 − 603,776) | 479,615 (436,219–1,161,385) | 742,436 (152,225–1,084,012) | 545,036 (296,662–1,096,067) |
No | 235,524 (121,928 − 362,918) | 559,329 (329,957 − 679,370) | 673,381 (448,337–914,674) | 355,981 (200,883 − 664,758) |